https://www.um.edu.mt/library/oar/handle/123456789/10993 2026-04-04T19:10:52Z https://www.um.edu.mt/library/oar/handle/123456789/11001 Title: 3 year old with chronic wet cough : Intralobar Bronchopulmonary sequestration Authors: Micallef, S.P.; DeGiovanni, Joseph V.; Grech, Victor E.; Sammut, Patrick Abstract: Bronchopulmonary sequestration (BPS) is a rare congenital foregut anomaly of the lung, consisting of nonfunctioning primitive tissue that does not communicate with the healthy tracheobronchial tree. The abnormal segment has its own anomalous systemic blood supply, and typically drains into the pulmonary venous system. It is frequently asymptomatic and may be discovered incidentally. Symptoms may vary, with patients presenting with vague symptoms related to chronic respiratory infection. Early diagnosis and intervention decreases morbidity and mortality. We present a case of intralobar pulmonary sequestration involving the right lower lobe in a male child. 2016-01-01T00:00:00Z https://www.um.edu.mt/library/oar/handle/123456789/11000 Title: Aortic arch tortuosity with PHACE syndrome : a rare case scenario Authors: Sharma, B.; Reddy, A.K.; Ganigara, M.; Baidwan, A.; Vyas, Y.S.; Rao, Nitin K. Abstract: PHACE syndrome is a rare neurocutaneous disorder characterised by an association of infantile haemangiomas with structural anomalies of brain, cerebral vasculature, eye, aorta and chest wall.1 Coarctation of aorta (COA) is most the common cardiac anomaly reported in PHACE syndrome. COA or interrupted aortic arch in PHACE is unique and complex both in location and character compared to the typical coarctation anatomy. Arterial tortuosity of the cerebral vasculature has been well described in literature in PHACE syndrome. We present a rare case of tortuous aortic arch continuing as descending aorta in an infant with PHACE syndrome. 2016-01-01T00:00:00Z