https://www.um.edu.mt/library/oar/handle/123456789/27483 2026-04-11T08:58:54Z https://www.um.edu.mt/library/oar/handle/123456789/4300 Title: Pulmonary valvulotomy in a fetus with pulmonary atresia with intact ventricular septum : first experience in Turkey Authors: Polat, Tugcin Bora; Danısman, N. Abstract: The mortality and morbidity of children with pulmonary atresia with intact ventricular septum (PA/IVS) is closely related with right ventricle hypoplasia and its consequent hemodynamics. Prenatal intervention for fetuses with PA/IVS has the potential to improve growth of the RV and the prospect of a biventricular outcome after birth. Successful valvulotomy of the pulmonary valve (PV) was performed in a fetus with PA/IVS at 28 weeks. Following the procedure there was an improvement in fetal hemodynamics. In utero perforation and dilation of the PV in midgestation fetuses with PA/IVS is technically feasible. The initial results are promising and may be associated with improved right heart growth and postnatal outcome. 2012-01-01T00:00:00Z https://www.um.edu.mt/library/oar/handle/123456789/4299 Title: Spontaneous subarachnoid haemorrhage due to coarctation of aorta and intraspinal collaterals : a rare presentation Authors: Devara, Anil K.V.; Joseph, S.; Uppu, S.C. Abstract: The occurrence of spontaneous subarachnoid haemorrhage (SAH) in association with coarctation of thoracic aorta and absence of intracranial aneurysm is a rare association. In spontaneous SAH, the predominant cause is intracranial aneurysmal rupture. This report describes a case of a 40 year-old male who presented with SAH and was incidentally diagnosed to have coarctation of aorta (CoA) with intraspinal collaterals on further work up. This case demonstrates the importance of detailed evaluation of patients with spontaneous SAH on whom common aetiologies have been ruled out. 2012-01-01T00:00:00Z https://www.um.edu.mt/library/oar/handle/123456789/4292 Title: Pacemaker-associated cyanosis in an adolescent : the answer hiding behind shadows Authors: Wittekind, S.G.; Salerno, Jack Christian; Rubio, Agustin E. Abstract: Lead thrombosis is a recognized complication of permanent transvenous pacemaker (PM) implantation. We present the interesting case of an adolescent with a dual-chamber PM presenting with fatigue and hypoxemia. Due to limitations of various imaging modalities, the diagnosis was difficult. She was eventually diagnosed with intracardiac PM lead thrombi obstructing tricuspid valve inflow. The pediatric literature on PM lead thrombosis is also briefly reviewed. 2012-01-01T00:00:00Z https://www.um.edu.mt/library/oar/handle/123456789/4285 Title: Gastric pseudoaneurysm in the setting of Loey’s Dietz Syndrome Authors: Likes, Maggie L.; Johston, Troy Alan Abstract: Loey’s Dietz syndrome is a disorder of connective tissue caused by a mutation in the genes that encode transforming growth factor (TGF) beta receptor 1 and 2. It is an autosomal dominant disorder similar to Marfan’s syndrome but with a more aggressive clinical course. Patients with Loey’s-Dietz syndrome have progressive dilatation of the aortic root that can lead to aortic dissection and rupture. The location of non-aortic arterial aneurysms may be wide spread but often occur in the head and neck vessels. 2012-01-01T00:00:00Z