https://www.um.edu.mt/library/oar/handle/123456789/3645 2026-04-23T17:24:02Z https://www.um.edu.mt/library/oar/handle/123456789/4270 Title: Isolated Biventricular Noncompaction in an adult with severe pulmonary hypertension : an association reviewed. Authors: Awasthy, Neeraj; Tomar, Munesh; Radhakrishnan, Sitaraman Abstract: Biventricular noncompaction is a recently recognized rare form of cardiomyopathy. It is characterized by altered structure of myocardial wall as a result of intrauterine arrest of compaction of the myocardial fibers in absence of coexisting congenital lesion. Left ventricle is the most affected site for noncompaction, but right ventricular involvement has been reported in a few cases. Diagnosis is made with 2-dimensional echocardiography or cardiac magnetic resonance imaging. While major clinical manifestations are heart failure, arrhythmias and embolic events,pulmonary artery hypertension ( PAH)has not been well elaborated in the literature. We present a 13- year old boy who had Biventricular noncompaction complicated by severe pulmonary hypertension. Pulmonary hypertension may be a consequence of increased pulmonary venous pressures caused by systolic and diastolic left ventricular dysfunction secondary to noncompaction. This article reviews the literature particularly with reference to PAH in the context of this case. 2012-01-01T00:00:00Z https://www.um.edu.mt/library/oar/handle/123456789/4269 Title: Cor triatriatum sinister with situs inversus totalis in an infant. Authors: Taksande, Amar M.; Gadekar, A.; Meshram, Sushant; Pathak, Swanand Abstract: Cor triatriatum sinister is a rare congenital cardiac malformation characterized by a membrane in the left atrium which separates the left atrium into the proximal and distal chambers.Association of cor triatriatum is extremely rare with situs inversus totalis. This article reports a rare case of cor triatriatum sinister with situs inversus totalis in a 5 month old female infant 2012-01-01T00:00:00Z