https://www.um.edu.mt/library/oar/handle/123456789/4317 2026-04-05T12:31:48Z https://www.um.edu.mt/library/oar/handle/123456789/4333 Title: An asymptomatic 11 year child with ruptured sinus of Valsalva Authors: Abqari, Shaad; Rabbani, Zeinab; Meshram, H. S.; Gupta, A. Abstract: Ruptured sinus of Valsalva (RSOV) is a rare lesion in a paediatric age group. A right sinus of Valsalva aneurysm usually ruptures into the right ventricle, while aneurysms of non-coronary sinus do so into the right atrium. RSOV usually presents in the third decade of life with congestive heart failure and is more common among Asians with male predominance. It may present as acute cardiogenic shock and sudden death or may remain completely asymptomatic with incidental detection by a murmur. Surgery is indicated as early as possible, once the diagnosis is made as without surgery, most cases will eventually succumb to uncontrollable congestive heart failure. This article reports an 11 year old child with the diagnosis of ruptured sinus of Valsalva. 2015-01-01T00:00:00Z https://www.um.edu.mt/library/oar/handle/123456789/4332 Title: Tetralogy of Fallot with absent pulmonary valve syndrome : an imaging challenge Authors: Keivanidou, Anastasia; Gogou, Maria; Giannopoulos, Andreas Abstract: Congenital absence of pulmonary valve syndrome (APV) represents a fascinating and unique variant of congenital heart disease. It was Chever in 1847 who first described this unique structural heart defect. The anatomic features consist of an incompletely formed, rudimentary pulmonary valve that is both stenotic and regurgitant, massively dilated pulmonary arteries and a large malaligned outlet ventricular septal defect. There is an association of this defect with Tetralogy of Fallot (ToF) due to which this condition is often referred to as Tetralogy of Fallot/absent pulmonary valve syndrome. Another characteristic feature is that there is virtually always absence of a patent ductus arteriosus. That has been hypothesized as being responsible for the pathogenesis of pulmonary artery dysplasia. 2015-01-01T00:00:00Z