Classical supravalvar aortic stenosis and peripheral pulmonary stenosis

Abstract

Supravalvar aortic stenosis as well as peripheral pulmonary stenosis are rare forms of congenital heart disease, which occur, however, relatively frequently in association. This article reports and discusses the classical findings of SVAS and PPS upon clinical examination and imaging in a sixyear-old girl that presented with repeated respiratory tract infections and failure to thrive.