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Title: Case number 3 : Prune Belly Syndrome aka Eagle Barrett Syndrome
Authors: Grima, Melanie
Mallia, Nicola
Keywords: Prune Belly Syndrome
Abnormalities, Multiple -- Diagnosis
Abnormalities, Human -- Case studies
Issue Date: 2015
Publisher: Malta Medical Students' Association
Citation: Grima, M., & Mallia, N. (2015). Case number 3 : Prune Belly Syndrome aka Eagle Barrett Syndrome. Minima Medicamenta, 4, 17-26.
Abstract: HM, male Severe bilateral hydronephrosis was noted at 20 weeks gestation with normal liquor at the time. The baby was delivered by elective C-section at 39 weeks gestation and very little liquor was noted. He was noted to have deficient abdominal wall musculature and cryptorchidism and prune-belly syndrome was suspected. A renal US confirmed bilateral severe hydroureteronephrosis with no evidence of posterior urethral valves or vesico-ureteric reflux on micturating cystourethrogram. A DTPA scan excluded outflow tract obstruction and a DMSA scan showed a non-functioning left kidney. His creatinine was noted to be 228umol/l (normal creatinine at this age 20-30umol/l). An ultrasound of the brain and back revealed no spinal anomalies and an echocardiogram showed a normal heart. Over the first few months of life he was managed conservatively on medications for chronic kidney disease. At the age of 1 year he underwent a left orchidopexy and a right first stage Fowler Stephen’s procedure. The second stage was performed a few months later.
Appears in Collections:Minima Medicamenta 2015
Minima Medicamenta 2015

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